Search on: G(M1) GANGLIOSIDE 
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Descriptor English:   G(M1) Ganglioside 
Descriptor Spanish:   Gangliósido G(M1) 
Descriptor Portuguese:   Gangliosídeo G(M1) 
Synonyms English:   GM1a Monosialoganglioside
Ceramide, Monosialosyl Tetraglycosyl
Monosialoganglioside, GM1a
Tetraglycosyl Ceramide, Monosialosyl
Monosialosyl Tetraglycosyl Ceramide  
Tree Number:   D09.400.410.420.025.475.390
D10.390.470.025.475.390
D10.570.877.360.025.475.390
Definition English:   A specific monosialoganglioside that accumulates abnormally within the nervous system due to a deficiency of GM1-b-galactosidase, resulting in GM1 gangliosidosis. 
History Note English:   86(77); was see under GANGLIOSIDES 1977-85 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AA analogs & derivatives
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
DF deficiency EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UR urine
Record Number:   5815 
Unique Identifier:   D005677 

Occurrence in VHL:
 

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